Primary amyloidosis presenting intrahepatic cholestasis and fulminant hepatic failure
نویسندگان
چکیده
منابع مشابه
Primary Amyloidosis Presenting with Nephrotic Syndrome and Atypical Intrahepatic Cholestasis: Report of 2 Cases
Liver is one of the most commonly involved organs in both primary and secondary systemic amyloidoses, but hepatic amyloidosis, manifested as mild to moderate enlargement, is usually not symptomatic nor it is clinically problematic. Rarely, massive hepatomegaly, severe cholestatic hepatitis or liver failure may be encountered in patients with systemic amyloidosis. Two cases with lambda light-cha...
متن کاملPrimary Hepatic Amyloidosis Presenting as Acute-on-Chronic Liver Failure
Systemic amyloidosis of amyloid light chain associated protein (AL), also called primary amyloidosis, frequently involves the liver, but rarely causes clinically apparent liver disease. The more common presentation is with acute renal failure. Hepatomegaly and mild elevation of alkaline phosphatase are the most common clinical and biochemical findings, respectively. We report a case of systemic...
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Background: Glyphosate containing herbicides are widely used the world over. They are marketed as nontoxic to humans, but numerous studies have showed that these glyphosate-based herbicides (GlySH) can cause multiorgan damage.1 Recent reports of animal studies on rats have raised a doubt of liver damage after long term exposure to GlySH. Case Presentation: a young male had chronic exposure to G...
متن کاملprimary hepatic amyloidosis with severe cholestasis: a case report
despite the fact that hepatic involvement is frequently seen in systemic primary amyloidosis, major hepatic symptoms as primary manifestation and severe impaired liver function are rare. herein, we report a 38-year-old woman with primary hepatic amyloidosis, and severe portal hypertension . the patient had ascites and markedly elevated alkaline phosphatase level at presentation. she had a rapi...
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A 9-month-old child presented with four days fever and altered sensorium for 2 days. He developed seizures in the emergency department and was in a state of shock. His blood sugar was 9 mg/dL. He was resuscitated with intravenous fluids. The child had fever, altered sensorium and erythematous skin. His liver was palpable 4 cm below right costal margin and spleen was just palpable. The limbs wer...
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ژورنال
عنوان ژورنال: Italian Journal of Medicine
سال: 2015
ISSN: 1877-9352,1877-9344
DOI: 10.4081/itjm.2015.593